There are three known variations in histology in the family of Embryonal tumour with multiple rosettes. This family incorporates embryonal tumor with plenteous neuropil and true rosettes (ETANTR), ependymoblastoma and medulloepithelioma. We report a case of 6-year-old child showing with highlight of expanded intracranial weight and found to have a cleared out parieto-occipital injury in brain. The patient experienced a sub-total extraction of the tumor and histopathology and immunohistochemistry was suggestive of ETANTR. Craniospinal irradiation (CSI) was arranged and amid treatment, patient developed numerous episodes of seizures and grade IV haematological toxicity amid radiotherapy and thus patient lapsed with overall survival of 5 month. We moreover performed a comprehensive outline in terms of clinical, pathological, molecular and management results of this uncommon entity of paediatric brain tumor.
